Chronic Septic Granulomatosis Revealed in Adulthood by Respiratory Manifestations

Authors

  • Fatima Ezzahra Haouassia Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco
  • Khadija Chaanoun Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco
  • Nahid Zaghba Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco
  • Hanane Benjelloun Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco
  • Najiba Yassine Pulmonology Department, Ibn Rochd University Hospital, Casablanca, Morocco

DOI:

https://doi.org/10.33533/jpm.v18i1.7554

Keywords:

immunodepression, immune disorder, respiratory infections, invasive aspergillosis, chronic septic granulomatosis

Abstract

Chronic septic granulomatosis is a rare genetic disease that affects the immune system. It is characterized by a primary immune deficiency that makes it more difficult for phagocytic cells (such as polymorphonuclear neutrophils, eosinophils, monocytes, and macrophages) to eradicate some harmful bacteria and fungi. It is considered an orphan disease because it affects less than 0.05% of a given population.

References

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Published

2024-06-15

How to Cite

Haouassia, F. E., Chaanoun, K., Zaghba, N., Benjelloun, H., & Yassine, N. (2024). Chronic Septic Granulomatosis Revealed in Adulthood by Respiratory Manifestations . Jurnal Profesi Medika : Jurnal Kedokteran Dan Kesehatan, 18(1), 112–118. https://doi.org/10.33533/jpm.v18i1.7554

Issue

Vol. 18 No. 1 (2024): Jurnal Profesi Medika : Jurnal Kedokteran dan Kesehatan

Section

Case Study

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